A Man Named Ludwig

By: Ilya Kott, M.D.
Emergency Medicine Resident
St. John Hospital and Medical Center

He was a bearded man in his fifties. An emesis basin clutched in his hands was rapidly filling with the oral secretions that he was unable to control. Every time he spoke it was obvious that he was in pain. His wife sat nearby. With worry etched on her face and fear in her voice she said, “He was seen just a couple hours ago and now it’s worse”.

A review of the previous chart was made. He had earlier presented with five days of right-sided submandibular swelling. A diagnosis of lymphadenitis was made and he was given a prescription for antibiotics and NSAIDS. The patient was not able to fill the prescription that night and returned to the emergency department now with difficulty with breathing and inability to control his own secretions.
The patient's past medical/surgical history was positive for hypertension, hypercholestrolemia, and an appendectomy. Further questioning also revealed that he had a recent toothache.

On exam, the patient’s vital signs were significant for a fever of 102.4 F and tachycardia of 112 BPM. His blood pressure and respiratory rate were normal. Oxygen saturation was 94%. General exam showed a mildly obese male in moderate distress. HEENT exam was positive for brawny edema of the neck; mild elevation of the tongue and the patient was unable to protrude his tongue. Cardiovascular, lung, abdominal and extremity exams were all normal.

Are all the symptoms due to the lymphadenitis, which is now worsening? Did the patient have a reaction to the medication given during his first visit? Was he misdiagnosed during his first visit?

As these considerations were being made, the patient was given IV solumedrol, benadryl, and pepcid. A CT scan of the neck was ordered as well as a CBC, electrolytes, glucose, BUN, and creatinine. Considering the rapid onset of the patient’s symptoms and the very real possibility of airway compromise the difficult airway equipment was prepared, the patient was given IV clindamycin and oralmaxillofacial surgery was called. This patient most likely had Ludwig’s angina and needed all these preparations urgently.

Ludwig’s Angina is a deep space dental infection, a cellulitis that may develop into an abscess, which requires airway management, operative drainage, and intravenous antibiotic treatment. Wilhelm Frederick von Ludwig first described it in 1836. Ironically he died at age 75, possibly from Ludwig’s angina. A true Ludwig's angina includes infection of the submandibular, sublingual, and submental spaces, but infection of even one space can be life threatening. Before the advent of antibiotics and the use of surgical decompression the mortality rate for Ludwig's angina was close to 50%. Today it is down to 10% if it is properly and promptly diagnosed and treated.

Etiology
Ludwig's angina has a male to female prevalence of 3:2. The floor of the mouth contains the mylohyoid muscle. It forms a sling by attaching to the two medial sides of the mandible. Superficial to the mylohyoid is the sublingual space. Deep to it is the submandibular space. Eighty percent of Ludwig's angina is caused by odontogenic disease or recent tooth extractions. Infections or extractions of the second or third molars are particularly at risk for developing Ludwig’s angina. The roots of these teeth extend below the mylohyoid ridge. Abscesses can therefore penetrate from there through the lingual plate and reach the submandibular spaces. Additional etiologies of Ludwig's angina include deep lacerations to the floor of the mouth, mandibular fractures, and salivary duct calculi.

Signs and symptoms
Symptoms include tooth pain, neck pain, difficulty in breathing, dysphagia, dysarthria, neck or chin swelling. Physical exam includes fever, an elevated tongue, brawny induration of the suprahyoid region, and trismus.

Complications
Prompt diagnosis of Ludwig's angina is crucial. Complications of the disease can be severe and deadly. The most immediate complication can be airway compromise. Further complications can include further spread of the submandibular infection to the mediastinum. From there it can then affect the great vessels and the pericardium as well as the lungs and pleural spaces.

Differential diagnoses
In order to make the diagnosis rapidly the differential diagnoses must be carefully considered and quickly excluded. The differential can include mandibular abscesses, neoplastic masses, or Lemiere's, a septic thrombophlebitis of the internal jugular vein. Each of these can be excluded by history or exam alone. Mandibular abscesses as well as Lemiere's are usually unilateral, Ludwig's angina will present with bilateral swelling. Tumors, although not always unilateral, can be excluded by history. Ludwig's has a rapid progression while tumors are usually slower growing.

Testing
Ludwig's angina is a clinical diagnosis. Laboratory and radiological testing are not necessary to make the diagnosis and instead can lead to a delay in diagnosis and ultimately treatment with disastrous outcomes.

Radiological imaging does play a role in delineating the extent of the infection allowing better decisions to be made in regards to surgical intervention. Before sending the patient for imaging studies it is imperative to secure the patients airway.

Treatment
Airway control should be the first concern in a Ludwig's patient. The swelling of the submandibular spaces with the subsequent elevation of the tongue, and the involvement of the epiglottis, can lead to airway compromise. The patient should be moved to the resuscitation area of the emergency department. Endotracheal intubation may not be possible and preparation for alternative means of airway control should be made. These can include nasotracheal or surgical airway approaches. Therefore the appropriate equipment (fiber optics, crichothyroidectomy kits) and personnel (surgery, anesthesia, or ENT) should be on hand when airway control begins.

Broad-spectrum antibiotics should be started on all patients. As mentioned above the mortality rate for Ludwig's angina before the advent of antibiotics was 50%. The most commonly cultured bacterial species are staphylococci, streptococci, and bactiroides. Klebsiella, H. influenza, Proteus and Pseudomonas are also prevalent and treatment should include coverage against those species as well. IV penicillin or a third-generation cephalosporin in combination with clindamycin or metronidazole for anaerobic coverage can be used.
About 50% of patients will improve with airway control and antibiotics alone. The other 50% percent will require surgical decompression and/or debridement of the submandibular spaces. No matter whether the patient gets antibiotics alone, or also requires airway protection and surgery, they should be sent to an ICU for close monitoring.

The patient never went for his CT scan. The results of the laboratory studies that were ordered had not even come back. The consulting physician did not need them. This patient had a clinical diagnosis of Ludwig’s angina. OMFS took the patient straight to the OR where he was fiberopticaly intubated. They then drained abscesses that had formed in the submental, sublingual, and submandibular spaces (a true Ludwig’s). Additionally they removed tooth # 17 which was thought to have been the initial source of infection. He stayed intubated and on IV unasyn until post op day #2 at which point the edema had gone down enough for him to be extubated. He was switched from Unasyn to Clindamycin and was finally discharged on PO clindamycin.

Swift proper diagnosis of Ludwig’s angina allowed this man to be properly treated with airway control, antibiotics, and surgical drainage. He got to be part of those ninety percent of patients who survive Ludwig’s angina with the proper treatment.


References:
Did Ludwig's angina kill Ludwig? J Laryngol Otol. 2006 May;120(5):363-5. Wasson J, Hopkins C, Bowdler D.
Tintinalli's Emergency Medicine:A Comprehensive Study Guide, 6e
Judith E. Tintinalli, MD, MS, Gabor D. Kelen, MD, J. Stephan Stapczynski, MD,
O. John Ma, MD and David M. Cline, MD

The Atlas of Emergency Medicine, 3e Kevin J. Knoop, Lawrence B. Stack, Alan B. Storrow, R. Jason Thurman
Emergency Medicine by James G. Adams MD FACEP, Erik D. Barton MD, Jamie Collings, and Peter M. DeBlieux MD (Jun 10, 2008)


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Posted:
Sunday, November 7, 2010

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